Free online searchable
2009 ICD-9-CM
Diseases and Injuries
>> Tabular
Index
>> Alphabetic
Index
Procedures
>> Tabular
Index
>>
Alphabetic Index
Appendices
>> Drugs
/ Chemicals
>> External Causes
Other Resources
>> HCPCS Alpha
>> Medical
Dictionary
>> Drug Directory
Tips
Contribute
| Wolman Disease Xanthomatosis, Familial | Xanthomatosis, Wolman' | s | Wolman' | s Disease | Disease, Wolman | Disease, Wolman' | s | Familial Xanthomatoses | Familial Xanthomatosis | Wolman' | s Xanthomatosis | Wolmans Disease | Xanthomatoses, Familial The severe infantile form of inherited lysosomal lipid storage diseases, due to deficiency of acid lipase. It results in accumulation of neutral lipids, particularly cholesterol esters, within cells (particularly leukocytes, fibroblasts, and liver cells). An allelic variant of CHOLESTEROL ESTER STORAGE DISEASE, it is also known as Wolman's xanthomatosis. |