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| 277 Other and unspecified disorders of metabolism |
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eicd10 | 277.1 Disorders of porphyrin metabolism
Hematoporphyria
Hematoporphyrinuria
Hereditary coproporphyria
Porphyria
Porphyrinuria
Protocoproporphyria
Protoporphyria
Pyrroloporphyria |
eicd10 | 277.2 Other disorders of purine and pyrimidine metabolism
Hypoxanthine-guanine-phosphoribosyltransferase deficiency [HG-PRT deficiency]
Lesch-Nyhan syndrome
Xanthinuria
Excludes: gout (274.0-274.9)
orotic aciduric anemia (281.4) |
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eicd10 | 277.4 Disorders of bilirubin excretion
Hyperbilirubinemia:
congenital
constitutional
Syndrome:
Crigler-Najjar
Dubin-Johnson
Gilbert's
Rotor's
Excludes: hyperbilirubinemias specific to the perinatal period (774.0-774.7) |
eicd10 | 277.5 Mucopolysaccharidosis
Gargoylism
Hunter's syndrome
Hurler's syndrome
Lipochondrodystrophy
Maroteaux-Lamy syndrome
Morquio-Brailsford disease
Osteochondrodystrophy
Sanfilippo's syndrome
Scheie's syndrome |
eicd10 | 277.6 Other deficiencies of circulating enzymes
Hereditary angioedema |
eicd10 | 277.7 Dysmetabolic syndrome X
Use additional code for associated manifestation, such as:
cardiovascular disease (414.00-414.07)
obesity (278.00-278.01) |
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eicd10 | 277.9 Unspecified disorder of metabolism
Enzymopathy NOS |